Porcelain Gall Bladder

 


Definition
Calcium based incrustation of gallbladder wall.
 
Radiographic Appearance
Plain abdominal image, the gall bladder is seen as having a translucent but semi radiolucent appearance, often seen co incidentally on IVU. and spine images
Non-functioning gallbladder on oral cholecystogram
Ultrasound highly echogenic shadowing curvilinear structure in the gallbladder fossa (stone-filled contracted GB)  echogenic gallbladder wall with little acoustic shadowing (emphysematous cholecystitis)
Scattered irregular clumps of echoes with posterior acoustic shadowing
 
Pathology
Extensive calcium encrustation of the gallbladder wall variably has been termed calcified gallbladder, calcifying cholecystitis, or cholecystopathia chronica calcarea. The term porcelain gallbladder has been used to emphasize the blue discoloration and brittle consistency of the gallbladder wall at surgery. Some authorities amalgamate the terms and call all calcified gallbladders porcelain gallbladders. The true incidence of porcelain gallbladder is unknown, but it is reported to be 0.6-0.8%, with a male-to-female ratio of 1:5. Most porcelain gallbladders (90%) are associated with gallstones.

Patients are usually asymptomatic, and porcelain gallbladder is found incidentally on plain abdominal radiographs, sonograms, or CT images. Surgical treatment of porcelain gallbladder is based on results from studies performed in 1931 and 1962, which revealed an association between porcelain gallbladder and gallbladder carcinoma. Porcelain gallbladder is uncommon, and recognizing the clinical and imaging characteristics of the disease is important because of the high frequency (22%) of adenocarcinoma in porcelain gallbladder. Surgery should not be delayed, even if the patient is asymptomatic, because the occurrence of carcinoma in porcelain gallbladder is remarkably high.


Pathophysiology: Histologically, flakes of dystrophic calcium exist within the chronically inflamed gallbladder wall. The muscular wall of the gallbladder undergoes fibrotic changes. Microliths are diffusely scattered throughout the mucosa, submucosa, and glandular spaces and in the Rokitansky-Aschoff sinuses. Calcification occurs in 2 forms: (1) a broad continuous band of calcification in the muscularis and (2) multiple punctate calcifications in the mucosa and glandular spaces of the mucosa. Gallstones are present in 90% of patients, hydrops obstructs the cystic duct. Most authorities consider gallbladder wall calcification to be secondary to a low-grade inflammation, but intramural hemorrhage and an imbalance in calcium metabolism also are implicated.
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Treatment:
Cholecystectomy recommended due to possibility of developing into a carcinoma.
 
Images of Porcelain gall bladder

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